Amit Bajpai, Manoj Sharma


Vein of Galen aneurysmal malformation (VGAM) is a rare congenital anomaly and amongst rare cause of congestive
heart failure in the neonatal period carrying high mortality rate. The diagnosis may remain elusive as the clinical picture
often mimics congenital cardiac malformation. Patients usually undergo high-risk procedures such as cardiac catheterization to establish a
diagnosis. Often, these investigations are inconclusive and can delay correct diagnosis. This study highlights the role of antenatal and follow up
Doppler USG which can lead to early diagnosis on the basis of characteristic Doppler ndings in a resource limited peripheral hospital. Various
therapeutic options for a VGAM include no treatment, endovascular treatment, open surgery and stereotactic radiosurgery. Timely diagnosis and
appropriate therapy especially endovascular management can result in fairly good outcome in these children.


Vein of Galen, Transcranial Ultrasound

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