DORSO-LUMBER INTRAMEDULLARY DERMOID CYST WITHOUT SPINAL DYSRAPHISM : A RARE ENTITY

Dr. Varun Aggarwal, Dr. Harman Sobti, Dr. Ashish Chhabra, Dr. Amit Narang

Abstract


Spinal dermoids are uncommon, especially in an intramedullary location. Absence of spinal dysraphism associated with
spinal dermoid is extremely rare and with best of our knowledge only seven cases have been reported in the literature till
date. This is a case of a 9-year-old boy, who presented with progressive weakness of both the lower limbs. Magnetic resonance imaging (MRI)
showed an intramedullary lesion extending from D11 to L1 with peripheral enhancement on contrast. Decompression of the cystic contents with
partial removal of cyst wall was done. Hair with sebum & fat was encountered. Histopathology confirmed the diagnosis of dermoid cyst. This case
adds to the previous reported cases of the rare and uncommon intramedullary space occupying lesions of the spinal cord.


Keywords


Spinal Dysraphism, Intramedullary Tumors, Intraspinal Dermoid Cysts

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References


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Lunardi P, Missori P, Gagliardi FM, et al. Long-term results of the surgical treatment of spinal dermoid and epidermoid tumors. Neurosurgery 1989;25:860-864


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