NOT ONLY A ROYAL DISEASE: HEMOPHILIA B (A CASE REPORT)

Dr Rounak Dubey, Dr Amit Biswas, Dr Amit Pawar

Abstract


Hemophilia B accounts for approximately 1 in 25000 births worldwide. Clinically Hemophilia A and B are indistinguishable. Both result in bleeding which lasts for a longer duration. Hemophilia is a group of X-linked recessive disorders wherein only the males are affected and females are carriers. Protracted bleeding after an invasive procedure may be the only manifestation in less severe forms. We present a case of moderate Hemophilia B diagnosed at a later age due to scarce diagnostic modalities, deficient family history of bleeding and lack of adequate awareness of the disease.

 


Keywords


Christmas disease,Hemophilia B,

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References


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